The Iron Man
Published: April 1, 2018 | DOI: https://doi.org/10.7860/JCDR/2018/32472.11416
Vikrant Vijan, Anjith Vupputuri, Aniketh Vijay Balegadde, Manav Aggarwal, Rajesh Thachathodiyl
1. Former Postgraduate, Department of Cardiology, Amrita Institute of Medical Sciences, Amrita Vishwa Vidyapeetham University, Kochi, Kerala, India.
2. Former Postgraduate, Department of Cardiology, Amrita Institute of Medical Sciences, Amrita Vishwa Vidyapeetham University, Kochi, Kerala, India.
3. Resident Interventional Cardiologist, Department of Cardiology, Amrita Institute of Medical Sciences, Amrita Vishwa Vidyapeetham University, Kochi, Kerala, India.
4. Former Postgraduate, Department of Cardiology, Amrita Institute of Medical Sciences, Amrita Vishwa Vidyapeetham University, Kochi, Kerala, India.
5. Professor, Department Of Cardiology, Amrita Institute of Medical Sciences, Amrita Vishwa Vidyapeetham University, Kochi, Kerala, India.
Correspondence
Dr. Vikrant Vijan,
Former Postgraduate, Department of Cardiology, Amrita Institute of Medical Sciences,
Amrita Vishwa Vidyapeetham University, Kochi-682041, Kerala, India.
E-mail: vikrantvijan@hotmail.com
The clinical presentation of haemochromatosis is usually complex and differs from patient to patient. We present one such complex case of primary haemochromatosis in a 35-year-old man with congestive heart failure and non-sustained ventricular tachycardia. He was a known case of diabetes, was infertile after nine years of marriage, and displayed haepatomegaly with increased homogenous attenuation of liver. His serum iron levels (347 µg/dL) and serum ferritin levels (2169 ng/mL) were very high, which made us call him an ‘Iron Man’. Liver biopsy and genetic testing confirmed the diagnosis of primary haemochromatosis. With regular phlebotomies, along with treatments for secondary complications, his symptoms improved gradually and the patient is doing well for past 11 years.
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